Angiotensin Converting Enzyme (ACE) for Gaucher Clinical Drug Monitoring
Label Mnemonic: GENACE
Epic code: LAB2593
Downtime form: A-1a Doctor/Provider Orders - Pathology Core and Specialty Care Nursery
Commercial Mailout Laboratory
6240-8 RCP
356-8593
Specimen(s):
Serum
Collection Medium:
Red top tube 5 mL (Clot Activator)
Minimum:
Adult Minimum: 2.0 mL serum
Pediatric Minimum: 1.0 mL serum
Rejection Criteria:
Specimens not received at reference laboratory within 4 days of specimen collection; do not collect on Fridays, holidays, day before a holiday, or weekends. Hemolyzed Specimens.
Turn Around Time:
7-14 days
Reference Range:
By report
Comments:
The Angiotensin converting enzyme assay uses tripeptide 
(hippuryl-his-leu) as subtrate and o-phthaldialdehyde for fluroescent 
derivatization.

Testing used for patients on Cerezyme (part of Gaucher Disease clinical 
drug monitoring including ACE, TRAP and CHITO).
Methodology:
Fluorometric Enzyme assay
CPT Code:
82164