The University of Iowa (UIHC)
Department of Pathology
LABORATORY SERVICES HANDBOOK


Chitotriosidase (CHITO) for Gaucher clinical drug monitoring
Order Code: GENCHITO
Epic Lab Code: LAB2845
Order Form: A-1a Miscellaneous Request or Epic Req
  Commercial "Mail-out" Laboratory
6240 RCP
356-3527
Specimen:
Serum
Collection Medium:
Red top tube
Minimum:
Preferred Pediatric minimum: 2.0 mL serum
Absolute Pediatric minimum: 1.0 mL serum
Rejection Criteria:
Specimens must be received at reference laboratory within 4 days of 
specimen collection; do not collect on Fridays, holidays, day before a 
holiday, or weekends.
Analytic Time:
1 week
Reference Range:
4 - 120 nmoles/hr/mL: median=22 nmoles/hr/mL
Comments:
The Chitotriosidase fluorometric enzyme assay uses 
4-methylumbelliferyl-beta-D-triacetylchitotrioside as substrate.

Testing used for patients on Cerezyme (part of Gaucher Disease clinical 
drug monitoring including ACE, TRAP and CHITO).
Methodology:
Fluorometric enzyme assay
CPT Code:
82657, 84155
 
See also:
Angiotensin Converting Enzyme (ACE) for Gaucher Clinical Drug Monitoring, Serum
Tartrate Resistant Acid Phosphatase (TRAP) for Gaucher clinical drug monitoring, Serum

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Updated: 07/11/2008

Note: The information contained in this handbook is for use by personnel of University of Iowa Health Care. No other use is implied or intended.