Pipecolic Acid
Label Mnemonic: PIPAPU
Epic Lab Code: LAB3860
Downtime Form: A-1a Doctor/Provider Orders - Pathology Core and Specialty Care Nursery
Commercial Mail-out Laboratory
5231 RCP
Random Urine
Collection Medium:
Yellow top round bottom tube (no additive)
Preferred Minimum: 5.0 mL from a random urine
Absolute Minimum: 2.0 mL
Turn Around Time:
4 weeks
Reference Range:
< or =30 days: < or =223.8 nmol/mg creatinine
31 days-5 months: < or =123.1 nmol/mg creatinine
6 months-11 months: < or =45.0 nmol/mg creatinine
> or =1 year: < or =5.7 nmol/mg creatinine
Interpretive Data:
Elevated pipecolic acid levels are seen in disorders of peroxisomal biogenesis; normal levels are seen in disorders with loss of a single peroxisomal function.
Patient's age is required on request form for processing.
Gas Chromatography-Mass Spectrometry (GC-MS)
CPT Code: